Head and Neck Imaging

Clinical and Radiologic Characteristics of Cleidocranial Dysplasis*

Author:ZOU Ya-nan, LIN Cong, TIAN Zhao-jian.

affiliation:Department of Oral and Maxillofacial Surgery, Shengli Oil-field Central Hospital, Dongying 257034, Shandong Province, China

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Abstract

Objective To investigate the clinical features and radiologic findings of cleidocranial dysplasis(CCD). Methods Two patients with a clinically verified CCD were reviewed retrospectively. Results All patients expressed developmental abnormality of crania, teeth and clavicle. The radiologic features of CCD are:①multiple impacted permanent and supernumerary teeth, hypoplastic maxillary sinus and slender coronoid process. ②open sutures of the skull, small maxillary sinuses, missing nasal bone, numerous wormian bones, large fontanelles, hypoplastic maxilla, and prognathic mandible. ③dysplasia of both the clavicles and cone shaped thorax. Conclusion Clinical and radiologic characteristics of CCD are distinctive in certain extent, wich help the diagnosis.

【Keyword】Cleidocranial Dysplasis; Radiography; Tomography; X-ray Computed

【Chart number】R445.3;R445.4;R681.1

【Document Identification Number】A

【DOI】10.3969/j.issn.1009-3257.2018.05.006