目的分析婴幼儿期SturgeWeber 综合征脑部CT特点。方法 将2012年1 月-2017年12月在我院确诊并有完整CT影 像学资料的63例Sturge-Weber综合征婴幼 儿列为回顾性分析对象，通过脑部CT影像 资料对婴幼儿SturgeWeber综合征受累部 位、病变脑叶密度、病变脑叶信号密度、 脑灰白质分界、脉络丛、脑萎缩形态及硬 膜下是否有出血或积液现象进行分析。结 果 63例患儿颅内均有典型钙化表现，主 要沿脑回、脑沟走行，34例呈曲线样、19 例呈条带状，10例呈迂曲条管状，其中颞 顶叶9例、顶叶10例、枕顶叶33例、额顶 11例，27例钙化灶区与颜面血管瘤同侧， 主要累及皮层；均可见局部脑沟、脑池及 蛛网膜下腔不同程度增宽；软脑膜血管瘤 同侧有不同程度的脑萎缩表现，表现为脑 室扩大、脑沟增宽、病变同侧大脑半球范 围大于钙化区，55例为局限性脑萎缩，其 余为广泛性脑萎缩；行增强CT扫描时可见 沿皮层表面走行的线样、脑回样强化，且 脑回状强化范围明显超出钙化灶范围，经 CTA可见畸形静脉影；31例CT增强扫描影 像可见侧脑室脉络丛明显增粗，且范围扩 大，强化明显；CT骨窗显示41例患儿与患 侧钙化脑组织毗邻的颅骨板障明显增厚； 32例可见血管畸形同侧硬膜下积液，均 无出血表现。结论 婴幼儿期SturgeWeber 综合征脑部CT以颅内局部钙化、软脑膜 血管瘤、局部脑萎缩为典型表现，提示 SturgeWeber综合征可能性，或可结合临 床表现、MRI等影像手段予以进一步确 诊。

Objective To analyze thebrain CT features of infantile Sturge-Weber syndrome. Methods Sixty-three infantswith Sturge-Weber syndrome diagnosed in the hospital from January 2012 to December 2017 and with complete CT imaging data were enrolled in the retrospective analysis. The involved sites, density of affected lobes, signal density of lobs, boundary of brain gray matter, choroid plexus, shape of brain atrophy, the presence of subdural hemorrhage or effusion were analyzed through brain CT imaging data of infantile Sturge-Weber syndrome. Results There were typical calcifications in brains of 63 children, mainly distributed along the gyrus and sulcus. 34 cases were curveshaped, 19 cases were ribbon shaped and 10 cases were curved tube shaped. Among them, there were 10 cases in the temporoparietal lobe, 33 cases in occipital parietal lobe and 11 cases in frontoparietal region. 27 cases of calcified foci were on the same side of the facial hemangioma, mainly involving the cortex. There was different degrees of widening in local sulcus, cisternand subarachnoid space. There was different degrees of brain atrophy on the same side of soft meningeal hemangiomas, manifesting as enlargement of the ventricles, widening of the sulci and cerebral hemisphere on the same side of lesions larger than calcified areas. 55 cases were focal brain atrophy, and the rest cases were extensive brain atrophy. Enhanced CT scanning showed line-like and gyrus-like enhancement on the surface of the cortex, and the extent of gyrus-likeenhancement was significantly larger than that of the calcified range. CTA showed abnormal venous shadow. CT enhanced scan of 31 cases showed obvious thickening of the lateral cerebral choroid plexus, and the scope expanded, with obvious enhancement. CT bone window showed obvious thickening of the skull adjacent to ipsilateral calcified brain tissues in 41 cases and subdural effusion on the same side of vascular malformations in 32 cases, without bleeding. Conclusion The typical CT features of infantile Sturge-Weber syndrome include intracranial local calcification, cerebral pia mater hemangioma and local brain atrophy, suggesting that CT combined with clinical manifestations and MRI can further confirm the diagnosis of Sturge-Weber syndrome.