目的 探讨CT尿路成像对泌尿系 统先天性发育畸形的价值。方法 回顾性 分析我院2014年1月-2016年1月期间接收 并经手术病理确诊的30例泌尿系统先天 畸形患者，行CT平扫、增强扫描、容积 (VR)重建，并对泌尿系统先天异常病种 特征进行综合分析。结果 泌尿系统肾 脏畸形病种中，肾脏异位12例，孤立肾 6例，肾异常旋转3例(盘状肾2例、马蹄 肾1例)，囊性不良发育肾6例，融合肾 畸形3例。重肾重输尿管畸形17例(单侧 重复肾重输尿管畸形13例、双侧重复肾 畸4例)。结论 CT平扫、增强扫描、容积 (VR)重建在对30例泌尿系统先天发育畸 形病种诊断过程中，全方位可靠的呈现 了病变之间的关系和解剖结构，发挥了 CT的优势，弥补其他影像学检查方法的 缺点，大程度的降低了临床上的漏诊率 和误诊率，对临床上的诊断和治疗提供 了指导意义。

Objective To investigate the value of CT urine road image formation on urinary system congenital abnormality. Methods 30 cases with urinary system congenital abnormality in our hospital from January 2014 to January 2016 were selected and given CT scan, enhancement scan, volume reconstruction. Analyze the congenital anomalies diseases of urinary system. Results In renal malformations diseases of urinary system, 12 cases ectopic kidney, 6 cases solitary kidney, 3 cases renal improper rotation (2 cases discoid kidney, 1 case horseshoe kidney), 6 cases cystic dysplasia kidney, 3 cases fused kidney, 17 cases double kidney with duplicate ureters (13 cases unilateral double kidney with duplicate ureters, 4 cases bilateral double kidney with duplicate ureters). Conclusion In the treatment of 30 cases with urinary system congenital abnormality, CT scan, enhancement scan and volume reconstruction can factually show mutual relation and anatomical structure of lesion. It can lower the missed diagnosis and misdiagnosis rate by large degree and provide guiding significance on clinic treatment.