目的 提高对原发性肺血管球瘤影像学表现的认识。方法 回顾性分析1例经手术病理证实为原发性肺血管球瘤患者 的CT表现，并做文献复习，总结其影像特点。结果 患者，男性，53岁，查体发现右肺病变。CT平扫表现为右肺中 叶直径3.8cm圆形肿块，边缘光整，CT增强扫描肿块周边呈不均匀明显强化，肿块中央强化不明显。结论 原发性肺 血管球瘤非常罕见，影像学无特征性表现，最终诊断有赖于组织病理学和免疫组织化学检查。

Objective To enhance the understanding of primary pulmonary glomus tumor involvement on radiological findings. Methods The CT findings of one case with primary pulmonary glomus tumor proven by pathology were retrospectively analyzed, and literature reviewed. Results A 53-year-old man was admitted to our hospital for an abnormal shadow in the right lung on a routine chest radiograph. Unenhanced CT showed a well-delineated round mass, 3.8cm in diameter, in the right medius lobe; no calcification or fat attenuation was seen. After injection of contrastmedium, the peripheral portion of the mass was markedly enhanced but the central portionwas poorly enhanced. Conclusion Primary pulmonary glomus tumor is very rare. Radiological investigation is helpful for localization of the tumor, and not specific. Pathological and immunohistochemical examination is required for considered in the diagnosis of primary pulmonary glomus tumor.