Objective To investigate the characteristics of CT enhancement scanning in patients with renal epithelioid angiomyolipoma. Methods Retrospective analysis of clinical and imaging data of 13 cases of renal epithelioid angiomyolipoma patients from January 2010 to June 2017, Review the relevant literature，To discuss the features of CT enhanced scanning image. Results 5 patients were misdiagnosed as renal cancer before surgery, 4 patients were correct before surgery, and 4 patients were diagnosed in the differential diagnosis. Clinical manifestations included abdominal pain, abdominal discomfort or physical examination.4 cases of larger tumors displayed as mixed density because it's contain a lot of fat , 9 cases of patients with CT for isodensity or slightly high density, 4 cases showed as "wedge" after three-d reconstruction, 9 caese were improved way as the "fast in slow out" type, 4 cases were improved way as the "fast forward fast" type, 5 cases of reinforcement are relatively uniform, 9 cases of strengthen the uneven. Conclusion The renal epithelioid angiomyolipoma is prone to misdiagnosis before surgery and has no specific clinical manifestations,Imaging findings is difficult to identify with kidney cancer,But when lesions on CT scan showed isodensity or slightly high density, 3 d reconstruction showed "wedge", enhanced scanning type is "fast in slow out", strengthen the extent is uniform, We should consider this disease.