Objective To study the CT and MRI findings of extra-abdominal desmoidtype fibromatoses and improve its diagnostic accuracy. Methods The data of 24 patients with pathologically proved extra-abdominal desmoid-type fibromatoses were collected. Among all the 24 cases,9 males and 15 females，median age is 46.5 years old.21 cases were primary，3 cases were secondary.10 cases underwent CT examination (2 cases with enhanced),20 cases MRI examination (15 case with enhanced),with both 6 patients. Image findings were evaluated in relation to the following: location, size, morphology, margin, CT density, MRI signal and enchancement pattern. Results Masses were located in limbs (14 cases), chest wall (4 cases), cervical part (2 cases)and buttocks (2 cases), sphenoid sinus (1 cases), paravertebral gutter(1 cases). Lesions were 1.9~11.2cm in size, including oval round masses in 6 cases and lobular masses in 18 cases, the majority (19/24) of lesions demonstrated ill defined circumscribed border. Neurovascular involvement was detected in 14 tumors (58.3%), periosteal adhesion was seen in 16 tumors (66.7%) and bone distruction was detected in 3 cases (12.5%).10 cases performed CT examinations , without necrosis and calcification, were slightly low density, 2 cases demonstrating moderate enhancement. Compared with the muscle signal, the lesions showed slightly low signal on T1WI and showed high and low mixed signal on T2 WI. After contrast enhancement, the lesions showed moderate enhancement. The stripe and patchy non-enhanced structures with low signal intensity on both T1WI and T2W1 were seen in 13 cases (65%). Conclusion Extra-abdominal desmoid-type fibromatoses is a rare intermediate soft tissue tumor. With the CT and MRI findings of lesions specific, CT and MRI examinations have important value in diagnosis and monitor after operation.