Objective To evaluate the diagnostic value of spiral CT and echocardiography of congenital vascular ring. Methods A retrospective analysis of January 2006 - January 2012 clinical data with congenital vascular rings of the 40 cases in our hospital, all patients underwent 64-slicespiral CT (Multi-slicespiral CT, MSCT), echocardiography (transthoracicechocardiography, TTE) examination, all patients were confirmed by surgery congenital vascular ring. The MSCT, TTE diagnosis and surgical diagnosis were compared, observed and compared MSCT and TTE examination of congenital vascular rings diagnosis rate and the combined cardiac malformations, tracheal stenosis, esophageal stenosis diagnosed cases. Results TTE and MSCT diagnosis of congenital vascular ring rates were 65.0%, 92.5%, TTE diagnosis and surgery was significantly lower than MSCT confirm the results, there is a big difference in comparison (χ2 =9.04,16.97, P<0.05), and MSCT examination of congenital vascular rings and surgically confirmed diagnosis rate were similar (P>0.05). MSCT congenital vascular rings with cardiac malformation, tracheal stenosis, esophageal stenosis diagnostic accuracy rates were 40.0%, 75.0%, 17.5%, significantly higher than the diagnostic accuracy of TTE examination (χ2 = 4.92,4.38,5.00, P<0.05), and the surgery to confirm the results more similar (P>0.05). Conclusion MSCT diagnosis of congenital vascular ring high accuracy, is basically consistent with the surgical diagnosis, both clearly shows the composition of vascular rings, but also clear the relationship between vascular rings and adjacent structures, can be combined as a congenital vascular TTE examination effective diagnostic tool ring, worthy of clinical application.