目的对先天性成人多囊肾的 CT、MRI影像学特征及与病理学进行对比 研究，为先天性成人多囊肾的影像诊断 提供理论依据。方法 本研究观察对象为 2014年1月-2017年1月于我院诊断与治疗 的100例先天性成人多囊肾患者，主要临 床表现为腹部肿块及血尿。所有患者均 进行CT及MRI检查，保留手术病理标本， 制作病理切片苏木素-伊红(HE)染色观察 病理切片，并与CT、MRI影像图像进行对 应比较。结果 所有患者均出现肾实质受 累，囊肿大小平均(43.34±6.45)mm；正 常肾脏实质被不同体积的囊肿所代替, 具有光滑的囊肿边缘，囊肿内密度均匀, CT值平均(7.43±1.21)Hu，增强扫描显 示囊肿部分间隔强化；MRI检查囊肿呈长 T1、T2信号, 其内部信号较为均匀。囊 内出血者显示囊肿内密度增高影，且可 不均匀, CT值平均(56.23±4.32)Hu；病 理检查结果显示囊壁附近有小结石，囊 肿伴钙化呈弧形或片状, 周围脏器因推 挤发生移位；病理检查显示囊肿壁以纤 维组织为主，部分可观察到肾小管上皮, 无肾组织正常结构。结论 多囊肾的CT、 MRI影像特征与其病理成分等相对应。

Objective To investigate the CT and MR imaging features of adult congenital polycystic kidney and comparison with pathology, and to provide a theoretical basis for the diagnosis of adult congenital polycystic kidney. Methods The clinical manifestations of 100 patients with adult congenital polycystic kidney treated in our hospital from Jan 2104 to Jan 2017 were abdominal mass and hematuria. All patients received CT and MRI examinations, the pathological sections were subjected to hematoxylin and eosin (HE) staining and pathologically observed and compared with the results of CT and MRI. Results All patients suffered the renal parenchymal involvement, the mean size of renal cyst was (43.34±6.45) mm, normal renal parenchyma was replaced by different volumes of cysts with a smooth edge and a uniform density, the mean CT value was (56.23±4.32) Hu, pathological examination showed small stones near the capsule wall, cyst with calcification was curved or lamellar, the surrounding organs were displaced. Pathological examination showed that the cyst wall was mainly composed of fibrous tissue, and tubular epithelium was observed, normal structure of kidney tissue was not founded. Conclusion The CT and MRI imaging features of polycystic kidney correspond to their pathological components.