目的 分析小儿先天性肺囊性腺 瘤畸形(CCAM)的CT征象及临床特点。方 法 选择2010年6月-2015年5月在我院经 手术病理确诊为CCAM的29例患儿。所有 患儿入院后均接受CT检查，且临床资料 完整，分析其临床表现，总结小儿CCAM 的CT影像学特点。结果 29例CCAM中，CT 检出右肺受累24例，其中上叶13例，下 叶9例，下中下叶受累2例；左肺受累5 例，上叶2例，下叶3例。其中23例为大 囊型，可见单发或多发薄壁气囊肿，内 部均可见不规则、多发线样分隔，囊周 肺组织无异常密度影；6例为小囊型，CT 可见蜂窝样变化，可见多个小囊，囊内 无气液平，囊肿附近肺组织无异常密度 影，无正常充气肺组织，纵膈可见右移 或无变化。结论 不同病理分型CCAM患儿 CT表现有其特殊性，CT分型与病理符合 度高，可作为CCAM筛选的重要手段。

Objective To analyze the CT findings and clinical features of congenital cystic adenomatoid malformation of the lung (CCAM) in children. Methods 29 cases of children who were diagnosed with CCAM by surgery and pathology in our hospital between June 2010 and May 2015 were enrolled in the study. All the children underwent CT examination after admission, and the clinical data were complete. The clinical manifestations were analyzed. The CT imaging findings of CCAM in children were summarized. Results Among 29 cases with CCAM, there were 24 cases with right lung involvement, including 13 cases of superior lobe, 9 cases of inferior lobe and 2 cases of inferior and middle lobe involvement detected by CT. There were 5 cases with left lung involvement, including upper lobe in 2 cases and lower lobe in 3 cases. Among them, 23 cases were large cystic type, with single or multiple thin wall air cysts. There were irregular and multiple line-like separations inside; 6 cases were follicular type. CT showed honeycomb-like changes and multiple cysts without intracystic gas-liquid free flat. There was no abnormal density shadow in lung tissues around cysts and no normal aerated lung tissues. There were presence of right shift of mediastinum or no changes. Conclusion The CT findings of children with different pathological types of CCAM are specific. The coincidence rate of CT typing and pathology is high, which can be used as an important means for screening CCAM.