目的 探讨腹壁韧带样型纤维瘤 病的CT和MR表现及病理基础，旨在提高对 本病的认识。方法 回顾性分析17例经手 术及病理证实的韧带样型纤维瘤病的影像 及病理结果。结果 17例病例共发现21个 病灶，其中单发15例，多发2例。病变位 于上腹壁5个，下腹壁16个。病灶呈梭形 或椭圆形18个，不规则形3个。其中16个 边界清楚，4个边界不清，1个部分不清。 浸润性生长5个，其中跨肌间隙3个；膨胀 性生长16个。CT检查，共发现病灶17个。 与肌肉密度对比，平扫呈等密度8个，稍 低密度8个，等低混杂密度1个。增强扫描 以中等以上渐进性强化为主，强化均匀 (12/17)，不均匀(5/17)。MRI检查发现病 灶4个，T1WI呈较均匀等信号，T2WI及其 脂肪抑制序列呈不均匀稍高或较高信号。 增强后呈不均匀显著强化，强化程度高于 肌肉。3例病灶内各序列见条带状低信号 影，增强后无明显强化。病理上肿瘤多由 纤维母细胞和肌纤维母细胞组成，内部见 致密纤维组织及胶原组织，常伴有灶性淋 巴细胞浸润、粘液样变性、玻璃样变性、 小血管增生扩张和出血。结论 腹壁韧带 样型纤维瘤病的CT和MRI表现有一定特征 性，反应了其病理特征，对本病诊断有重 要价值。

Objective To investigate the CT and MRI features and pathologic basis of abdominal desmoid-type fibomatoses and improve the understanding of the disease. Methods The images and pathologic results of 17 DF cases proved by sugery and pathology were retrospectively analyzed. Results 21 lesions were foud in 17cases,among which 15 cases were single and 2 cases were multiple. 5 Lesions were located in the abdominal wall and 16 lesions were located under the abdominal wall. 18 lesions displayed fusiform or elliptic and three lesions were irregular shape.The border of 16 lesions were clear,4 lesions were unclear,and One lesion was not clear.5 focuses grew aggressively, 3 of which crossed the muscle clearance,while 16 lesions grew expansicely.17 lesions were found on CT, among which 8 lessions were equal to the density of muscle,and 8 were slightly lower than the density of muscle ,1 was mixed density .Most lesions exhibited gradually moderate or obvious enhancement on post-contrast CT.12/17 were homogeneous, 5/17 were heterogeneous. 4 lesions were foud on MRI, which were homogeneous signals on TIWI and high signals or slightly higher signals on T2WI and Fat suppression. The lesions were uneven significant enhancement,The degree of strengthen was higher than the muscle. 3 cases of lesions foud low band signal in each sequence and without reinforcement on post-contrast MRI. Tumor was composed of fibroblasts and myofibroblasts on pathologically,among which fibrous tissue and collagen tissue were found, accompanied by focal lymphocytic infiltration, myxoid degeneration, hyaline degeneration, hyperplasia of small vessel expansion and bleeding. Conclusion Abdominal DF has some characteristics which reflected its pathological characteristics on CT and MRI, CT and MRI has important significance for its diagnosis.