目的 分析先天性支气管发育不 良的多层螺旋CT表现及临床诊断价值。方 法 回顾性分析2011年6月-2015年5月于我 院行多层螺旋CT检查的64例先天性支气管 发育不良患儿的临床资料，总结其影像学 特点，评估其诊断价值。结果 先天性支 气管肺囊肿CT可见圆形、卵圆形块状影， 密度均匀，厚度一致，边缘光滑；先天性 肺叶肺气肿CT扫描可见大叶内含气量上 升，肺叶透亮度提升，肺纹理、气管及心 脏向左偏移，邻近正常的肺组织被压缩； 先天性支气管闭锁CT可见左上肺叶尖后段 支气管开口处于闭锁状态，自肺门至肺叶 内可见放射状柱状征，呈“V”形，可见 支气管被黏液填塞、截断，周围肺组织肺 气肿。结论 采用螺旋CT诊断先天性支气 管发育不良，可显示支气管病灶位置及其 与邻近器官的关系，图像质量好，定性、 定位优势好。

Objective To analyze the findings and clinical value of multi-slice spiral CT in the diagnosis of congenital bronchial dysplasia. Methods The clinical data of 64 cases of children with congenital bronchial dysplasia who underwent multi-slice spiral CT in our hospital from June 2011 to May 2015 were retrospectively analyzed. The imaging findings were summarized and the diagnostic value was evaluated. Results CT of congenital bronchopulmonary cyst showed round or oval mass shadows, homogeneous density, uniform thickness and smooth edge; CT scan of congenital lobar emphysema showed increase of entrained air content in big lobe, improvement of radiolucency of lung lobe, lung markings, trachea and heart shifting to the left and compressed lung tissues close to normal pulmonary tissues; CT of congenital bronchial atresia showed that the bronchial opening of top-left lung lobe tip of posterior segment was in closed state. From hilus pulmonis to intra-lung lobe, there were radiating columnar signs, in V shape and bronchus was packed and cut off by mucus. There was lung emphysema in the surrounding lung tissues. Conclusion In the clinical diagnosis of congenital bronchial dysplasia, the application of multi-slice spiral CT combined with its post-processing technique can clearly show the location of bronchial lesions and its relationship with adjacent organs. The image quality is good. The qualitative and positioning advantages are significant